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Metabolic myopathiesMetabolic myopathies are disorders of muscle energy production that result in skeletal muscle dysfunction. Cardiac and systemic metabolic dysfunction may coexist. Symptoms are often intermittent and provoked by exercise or changes in supply of lipid and carbohydrate fuels. Specific disorders of lipid and carbohydrate metabolism in muscle are reviewed. Evaluation often requires provocative exercise testing. These tests may include ischemic forearm exercise, aerobic cycle exercise, and 31P magnetic resonance spectroscopy with exercise.
Document ID
20050000295
Acquisition Source
Legacy CDMS
Document Type
Reprint (Version printed in journal)
Authors
Martin, A.
(Neuromuscular Center, Presbyterian Hospital of Dallas TX 75231)
Haller, R. G.
Barohn, R.
Blomqvist, C. G.
Date Acquired
August 22, 2013
Publication Date
November 1, 1994
Publication Information
Publication: Current opinion in rheumatology
Volume: 6
Issue: 6
ISSN: 1040-8711
Subject Category
Life Sciences (General)
Report/Patent Number
ISSN: 1040-8711
Distribution Limits
Public
Copyright
Other
Keywords
Review
Review, Tutorial
Non-NASA Center
NASA Discipline Cardiopulmonary
Muscular Diseases/diagnosis/metabolism
Carnitine/metabolism
Magnetic Resonance Spectroscopy
Muscle, Skeletal/metabolism
Human
Myocardium/metabolism
Energy Metabolism
Glycogen Storage Disease/metabolism
Exercise Test

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